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  1. ICD-10-CM Home
  2. Chapter 4
  3. E70-E88
  4. E71.5

E71.5

Peroxisomal disorders

Non-billableCategory

Code Hierarchy

E71E71.5

Chapter: 4. Endocrine, nutritional and metabolic diseases

Section: E70-E88 - Metabolic disorders

Coding Guidelines

Excludes1 (Mutually Exclusive)

These codes should never be used together with E71.5

  • G37.0 - Schilder's disease (G37.0)

Specific Codes (5)

E71.50Billable

Peroxisomal disorder, unspecified

E71.51Category

Disorders of peroxisome biogenesis

E71.52Category

X-linked adrenoleukodystrophy

E71.53Billable

Other group 2 peroxisomal disorders

E71.54Category

Other peroxisomal disorders

Related Codes

E71.0Billable

Maple-syrup-urine disease

E71.1Category

Other disorders of branched-chain amino-acid metabolism

E71.2Billable

Disorder of branched-chain amino-acid metabolism, unspecified

E71.3Category

Disorders of fatty-acid metabolism

E71.4Category

Disorders of carnitine metabolism

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