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  1. ICD-10-CM Home
  2. Chapter 4
  3. E70-E88
  4. E71.0

E71.0

Maple-syrup-urine disease

Billable

Code Hierarchy

E71E71.0

Chapter: 4. Endocrine, nutritional and metabolic diseases

Section: E70-E88 - Metabolic disorders

Related Codes

E71.1Category

Other disorders of branched-chain amino-acid metabolism

E71.2Billable

Disorder of branched-chain amino-acid metabolism, unspecified

E71.3Category

Disorders of fatty-acid metabolism

E71.4Category

Disorders of carnitine metabolism

E71.5Category

Peroxisomal disorders

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