Systemic connective tissue disorders
101 codes in this section
Codes
Polyarteritis nodosa and related conditions
5 subcategoryies
Polyarteritis nodosa
Polyarteritis with lung involvement [Churg-Strauss]
Juvenile polyarteritis
Mucocutaneous lymph node syndrome [Kawasaki]
Other conditions related to polyarteritis nodosa
Other necrotizing vasculopathies
10 subcategoryies
Hypersensitivity angiitis
Thrombotic microangiopathy
3 subcategoryies
Thrombotic microangiopathy, unspecified
Hematopoietic stem cell transplantation-associated thrombotic microangiopathy [HSCT-TMA]
Other thrombotic microangiopathy
Lethal midline granuloma
Wegener's granulomatosis
2 subcategoryies
Wegener's granulomatosis without renal involvement
Wegener's granulomatosis with renal involvement
Aortic arch syndrome [Takayasu]
Giant cell arteritis with polymyalgia rheumatica
Other giant cell arteritis
Microscopic polyangiitis
Other specified necrotizing vasculopathies
Necrotizing vasculopathy, unspecified
Systemic lupus erythematosus (SLE)
4 subcategoryies
Drug-induced systemic lupus erythematosus
Systemic lupus erythematosus with organ or system involvement
7 subcategoryies
Systemic lupus erythematosus, organ or system involvement unspecified
Endocarditis in systemic lupus erythematosus
Pericarditis in systemic lupus erythematosus
Lung involvement in systemic lupus erythematosus
Glomerular disease in systemic lupus erythematosus
Tubulo-interstitial nephropathy in systemic lupus erythematosus
Other organ or system involvement in systemic lupus erythematosus
Other forms of systemic lupus erythematosus
Systemic lupus erythematosus, unspecified
Dermatopolymyositis
4 subcategoryies
Juvenile dermatomyositis
5 subcategoryies
Juvenile dermatomyositis, organ involvement unspecified
Juvenile dermatomyositis with respiratory involvement
Juvenile dermatomyositis with myopathy
Juvenile dermatomyositis without myopathy
Juvenile dermatomyositis with other organ involvement
Other dermatomyositis
5 subcategoryies
Other dermatomyositis, organ involvement unspecified
Other dermatomyositis with respiratory involvement
Other dermatomyositis with myopathy
Other dermatomyositis without myopathy
Other dermatomyositis with other organ involvement
Polymyositis
4 subcategoryies
Polymyositis, organ involvement unspecified
Polymyositis with respiratory involvement
Polymyositis with myopathy
Polymyositis with other organ involvement
Dermatopolymyositis, unspecified
5 subcategoryies
Dermatopolymyositis, unspecified, organ involvement unspecified
Dermatopolymyositis, unspecified with respiratory involvement
Dermatopolymyositis, unspecified with myopathy
Dermatopolymyositis, unspecified without myopathy
Dermatopolymyositis, unspecified with other organ involvement
Systemic sclerosis [scleroderma]
5 subcategoryies
Progressive systemic sclerosis
CR(E)ST syndrome
Systemic sclerosis induced by drug and chemical
Other forms of systemic sclerosis
4 subcategoryies
Systemic sclerosis with lung involvement
Systemic sclerosis with myopathy
Systemic sclerosis with polyneuropathy
Other systemic sclerosis
Systemic sclerosis, unspecified
Other systemic involvement of connective tissue
10 subcategoryies
Sjögren syndrome
13 subcategoryies
Sjögren syndrome, unspecified
Sjögren syndrome with keratoconjunctivitis
Sjögren syndrome with lung involvement
Sjögren syndrome with myopathy
Sjögren syndrome with tubulo-interstitial nephropathy
Sjögren syndrome with inflammatory arthritis
Sjögren syndrome with peripheral nervous system involvement
Sjögren syndrome with central nervous system involvement
Sjögren syndrome with gastrointestinal involvement
Sjögren syndrome with glomerular disease
Sjögren syndrome with vasculitis
Sjögren syndrome with dental involvement
Sjögren syndrome with other organ involvement
Other overlap syndromes
Behçet's disease
Polymyalgia rheumatica
Diffuse (eosinophilic) fasciitis
Multifocal fibrosclerosis
Relapsing panniculitis [Weber-Christian]
Hypermobility syndrome
Other specified systemic involvement of connective tissue
2 subcategoryies
Multisystem inflammatory syndrome
Other specified systemic involvement of connective tissue
Systemic involvement of connective tissue, unspecified
Systemic disorders of connective tissue in diseases classified elsewhere
6 subcategoryies
Dermato(poly)myositis in neoplastic disease
Arthropathy in neoplastic disease
Hemophilic arthropathy
Arthropathy in other blood disorders
Arthropathy in hypersensitivity reactions classified elsewhere
Systemic disorders of connective tissue in other diseases classified elsewhere
