Certain disorders involving the immune mechanism
100 codes in this section
Codes
Immunodeficiency with predominantly antibody defects
10 subcategoryies
Hereditary hypogammaglobulinemia
Nonfamilial hypogammaglobulinemia
Selective deficiency of immunoglobulin A [IgA]
Selective deficiency of immunoglobulin G [IgG] subclasses
Selective deficiency of immunoglobulin M [IgM]
Immunodeficiency with increased immunoglobulin M [IgM]
Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia
Transient hypogammaglobulinemia of infancy
Other immunodeficiencies with predominantly antibody defects
Immunodeficiency with predominantly antibody defects, unspecified
Combined immunodeficiencies
10 subcategoryies
Severe combined immunodeficiency [SCID] with reticular dysgenesis
Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
Adenosine deaminase [ADA] deficiency
4 subcategoryies
Adenosine deaminase deficiency, unspecified
Severe combined immunodeficiency due to adenosine deaminase deficiency
Adenosine deaminase 2 deficiency
Other adenosine deaminase deficiency
Nezelof's syndrome
Purine nucleoside phosphorylase [PNP] deficiency
Major histocompatibility complex class I deficiency
Major histocompatibility complex class II deficiency
Other combined immunodeficiencies
3 subcategoryies
Biotin-dependent carboxylase deficiency
3 subcategoryies
Biotinidase deficiency
Other biotin-dependent carboxylase deficiency
Biotin-dependent carboxylase deficiency, unspecified
Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]
Other combined immunodeficiencies
Combined immunodeficiency, unspecified
Immunodeficiency associated with other major defects
7 subcategoryies
Wiskott-Aldrich syndrome
Di George's syndrome
Immunodeficiency with short-limbed stature
Immunodeficiency following hereditary defective response to Epstein-Barr virus
Hyperimmunoglobulin E [IgE] syndrome
Immunodeficiency associated with other specified major defects
Immunodeficiency associated with major defect, unspecified
Common variable immunodeficiency
5 subcategoryies
Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function
Common variable immunodeficiency with predominant immunoregulatory T-cell disorders
Common variable immunodeficiency with autoantibodies to B- or T-cells
Other common variable immunodeficiencies
Common variable immunodeficiency, unspecified
Other immunodeficiencies
4 subcategoryies
Lymphocyte function antigen-1 [LFA-1] defect
Defects in the complement system
Other specified immunodeficiencies
3 subcategoryies
Immunodeficiency due to conditions classified elsewhere
Immunodeficiency due to drugs and external causes
2 subcategoryies
Immunodeficiency due to drugs
Immunodeficiency due to external causes
Other immunodeficiencies
Immunodeficiency, unspecified
Sarcoidosis
6 subcategoryies
Sarcoidosis of lung
Sarcoidosis of lymph nodes
Sarcoidosis of lung with sarcoidosis of lymph nodes
Sarcoidosis of skin
Sarcoidosis of other sites
8 subcategoryies
Sarcoid meningitis
Multiple cranial nerve palsies in sarcoidosis
Sarcoid iridocyclitis
Sarcoid pyelonephritis
Sarcoid myocarditis
Sarcoid arthropathy
Sarcoid myositis
Sarcoidosis of other sites
Sarcoidosis, unspecified
Other disorders involving the immune mechanism, not elsewhere classified
7 subcategoryies
Polyclonal hypergammaglobulinemia
Cryoglobulinemia
Hypergammaglobulinemia, unspecified
Immune reconstitution syndrome
Mast cell activation syndrome and related disorders
6 subcategoryies
Mast cell activation, unspecified
Monoclonal mast cell activation syndrome
Idiopathic mast cell activation syndrome
Secondary mast cell activation
Hereditary alpha tryptasemia
Other mast cell activation disorder
Other specified disorders involving the immune mechanism, not elsewhere classified
5 subcategoryies
Graft-versus-host disease
4 subcategoryies
Acute graft-versus-host disease
Chronic graft-versus-host disease
Acute on chronic graft-versus-host disease
Graft-versus-host disease, unspecified
Autoimmune lymphoproliferative syndrome [ALPS]
Cytokine release syndrome
6 subcategoryies
Cytokine release syndrome, grade 1
Cytokine release syndrome, grade 2
Cytokine release syndrome, grade 3
Cytokine release syndrome, grade 4
Cytokine release syndrome, grade 5
Cytokine release syndrome, grade unspecified
IgG4-related disease
Other specified disorders involving the immune mechanism, not elsewhere classified
Disorder involving the immune mechanism, unspecified
