M04.8
Other autoinflammatory syndromes
Billable
Code Hierarchy
M04M04.8
Coding Guidelines
Inclusion Terms
- Blau syndrome
- Deficiency of interleukin 1 receptor antagonist [DIRA]
- Majeed syndrome
- Periodic fever, aphthous stomatitis, pharyngitis, and adenopathy syndrome [PFAPA]
- Pyogenic arthritis, pyoderma gangrenosum, and acne syndrome [PAPA]


